Abnormal parahisian accessory pathway radiofrequency ablation in a patient with left ventricular noncompaction

Abstract

Left ventricular noncompaction (LVNC) is a rare primary genetic cardiomyopathy, due to the arrest of normal embryogenesis of the endocardium and myocardium (between the 5th and 8th weeks of gestation), developing multiple prominent hypertrabeculations with deep intertrabecular recesses reported primarily in the left ventricular chamber. The diagnosis is made more frequently between 20-40 years. Patients may remain asymptomatic or present a variable clinical expression. This anomaly is frequently associated with heart failure, arrhythmias and thromboembolic complications. The electrocardiogram does not present a specific diagnostic pattern, and electrocardiographic changes are frequent. Case reports have been reported associated with Wolff-Parkinson-White syndrome (WPW). We report a 27-year-old patient with noncompaction cardiomyopathy associated with WPW
syndrome, with symptomatic episodes of regular paroxysmal palpitations, with an accessory pathway located in the parahisian region, successfully ablated with RF energy.